An eight-year-old boy presented with a history of severs neck pain radiating to the right shoulder for one week. A well circumferential intra-dural extra-medullary mass arising from the dura on the right antero-lateral side of the spinal Cord was seen on magnetic resonance imaging. There was a high intensity dural tail above and below the mass associated and eccentric thickening of adjacent dura of persisting low signal in different images. Surgical exploration revealed a firm pinkish gray, hypovascular mass abutted the dura extending into the right C4 foramina .The dura was thickened not only at the origin of the mass but also a few segment above then and below the lesion. Pathological examination of the tumor revealed enterobius vermicularis inflamatory mass .This report is to our knowledge the first intradural–extramedullary presentation of oxyuriasis .Possible hematogenous mode of involvement of the CSF may further be supported by the present case.